Patient's question:
Is the book "Special Dietary Treatment for Phenylketonuria" still available in the market?Doctor's answer:
Hello! For newly diagnosed children, doctors and nutritionists should formulate diets for them. Parents with a certain level of education should learn to formulate diets themselves. Since parents live with their children, they understand their dietary habits and overall condition better than doctors and nutritionists. School-aged children should be taught to calculate their own diets and develop a positive and proactive habit of controlling their diet.Recommendations:
1. Based on age and weight, refer to the recommended intake to calculate the daily requirements for protein, phenylalanine, and energy. The majority of the total protein intake should come from special nutritional foods—phenylalanine-free milk powder (Nengquan Special TMXP-1, Nengquan Special TMXP-2)—with only a small portion coming from natural protein.
2. Breastfeeding is also recommended for children with phenylketonuria. Breast milk is the most nutritionally complete food and has the lowest phenylalanine content (about 36 mg per 100 ml of breast milk). Therefore, breast milk should be mixed with special milk powder (Nengquan Special) for feeding. Breast milk is the primary source of phenylalanine for infants, and infants without breast milk should be given calculated amounts of infant formula to ensure an adequate supply of phenylalanine for physiological needs.
Lifestyle Care:
During dietary therapy, blood phenylalanine levels must be carefully monitored. Newly formulated or adjusted diets should be tested for blood phenylalanine levels 5, 7, and 10 days after consumption to determine their suitability. Blood phenylalanine levels should be kept within the ideal range but not below 2 mg/dL (120 mmol/L). If the level falls below 2 mg/dL (120 mmol/L), it indicates a lack of phenylalanine in the body. A deficiency in phenylalanine disrupts the normal synthesis of new proteins in the body, leading to malnutrition and anemia. During dietary therapy, even if blood phenylalanine levels return to the normal range, at least one test should be conducted each month.
Wishing you good health!