Patient's question:
The patient underwent an ECT scan 70 days ago, with normal liver imaging and no visualization of the gallbladder. Subsequently, a laparoscopy revealed biliary atresia, with no visualization of the intrahepatic bile ducts or the left and right hepatic ducts. Partial visualization of the distal common bile duct and the main pancreatic duct was observed. The Kasai procedure was not performed. Currently at 100 days, the patient's mental state and weight are normal. Are there any other salvage measures available?Doctor's answer:
This is congenital biliary dyskplasia, characterized by significant liver enlargement. Under microscopic examination, most portal venous areas lack bile ducts, and bile duct dysplasia is sometimes observed, with many ducts lacking distinct lumens. Testicular interstitial fibrosis may also occur. It may develop, with mild jaundice occurring within 3 months after birth. Intrahepatic bile stasis is the main feature of this condition. Without special treatment, cholestyramine or traditional Chinese medicine can be taken to treat bile stasis and supplement fat-soluble vitamins.