Patient's question:
Half a year agoDoctor's answer:
It can also lead to sensory neural hearing loss, which is diagnosed through CT. The degree of hearing loss associated with labyrinthine malformations varies from none to complete, and it can be stable, fluctuating, and progressive. This hearing loss may contain a conductive component. A group of X-linked inherited labyrinthine malformations includes damage to the oval window, where affected children present with congenital conductive hearing loss. Surgical fenestration of the oval window can result in significant cerebrospinal fluid loss, often accompanied by persistent hearing impairment in that ear.